Both male/female patients with Fabry disease (FD) may receive enzyme replacement therapy (ERT). Previously published analyses of the Fabry Outcome Survey (FOS; Shire-sponsored) database suggested gender differences in timing of ERT initiation. We assessed alignment of criteria for ERT initiation in the Spanish adult population included in FOS with recommendations of a Spanish national consensus. This retrospective analysis examined baseline clinical data of 88 adults (49 females) enrolled in the FOS database up to August 2014.
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We report data from a prospective, observational study (ZAGAL) evaluating miglustat 100mg three times daily orally. in treatment-naïve patients and patients with type 1 Gaucher Disease (GD1) switched from previous enzyme replacement therapy (ERT). Clinical evolution, changes in organ size, blood counts, disease biomarkers, bone marrow infiltration (S-MRI), bone mineral density by broadband ultrasound densitometry (BMD), safety and tolerability annual reports were analysed. Between May 2004 and April 2016, 63 patients received miglustat therapy; 20 (32%) untreated and 43 (68%) switched.
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Listado de publicaciones generadas por el Registro Nacional de Insuficiencia Cardiaca (RICA)
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Esta Vía Clínica de Colecistitis Aguda ha sido realizada por iniciativa de los profesionales de las Unidades de Gestión Clínica de Cirugía General y Aparato Digestivo (HUR y HUM), de Medicina Integral (HUR y HUM), de Cuidados Críticos y Urgencias (HVR, HVM), de Enfermedades Infecciosas, Microbiología y Medicina Preventiva (HVR, HVM), de Radiodiagnóstico y Medicina Nuclear y de Enfermedades Digestivas (HVR y HVM).
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- Patterson JH, Adams KF Jr. Investigating the Role of Thiazide-Like Diuretics in Acute Heart Failure: Potential Approach to an Unmet Need. J Card Fail. 2016 May 12. pii: S1071-9164(16)30068-9. --- ENLACE
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Propuesta de indicadores para evaluar la atención a la cronicidad en el marco de la Estrategia para el Abordaje de la Cronicidad en el Sistema Nacional de Salud. Informe de evaluación de tecnologías sanitarias.
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Se acaba de publicar en España la decimonovena edición del manual Harrison: Principios de Medicina Interna, obra de referencia para estudiantes y profesionales de la salud.
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